Abstract:
Isolated ventricular non-compaction (IVNC) is an
under diagnosed familial cardiomyopathy which is
frequently misdiagnosed as dilated or hypertrophic
cardiomyopathy1,2. Awareness of this condition is
important because the outcome in infants is not
invariably fatal. We report an infant of Sri Lankan
parentage with isolated ventricular non-compaction
whose older sibling had died during infancy with a
diagnosis of ‘dilated cardiomyopathy
